Hearing Loss Autosomal Dominant 74 C4748334
A genetic hearing loss passed from one parent. It affects males and females equally. Hearing aids and other devices help manage the condition.
Key facts at a glance
- ICD-10
- Q17.9
- ICD-11
- LA00.0
- Body system
- otolaryngologic
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(otolaryngologic)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Post-lingual hearing loss
(otolaryngologic)Reduced speech discrimination
(otolaryngologic)Need for increased volume on electronic devices
(otolaryngologic)Tinnitus with hearing loss
(otolaryngologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Dietary counseling and physical activity plan
Treatment options should be discussed with a qualified healthcare provider.
Prescription Hearing Aid Management
Individually programmed hearing aids represent the cornerstone of management for autosomal dominant hearing loss. Regular follow-up visits ensure proper function and appropriate amplification as hearing changes over time.
Comprehensive Auditory Rehabilitation
Multimodal therapy combining listening exercises, communication practice, and cognitive strategies to maximize functional hearing. Programs may include both individual sessions and group workshops.
Additional treatment options
Middle Ear Implant System
Surgically placed active middle ear implants vibrate the ossicles or directly stimulate the cochlea. Indicated for patients who cannot use conventional hearing aids due to ear canal issues or specific types of hearing loss.
surgicalAntioxidant and Nutrient Support
General nutritional support with antioxidants and essential nutrients may provide modest protection for remaining auditory function. Focus on foods rich in folate, magnesium, and omega-3 fatty acids.
dietarySerial Audiological Assessment
Ongoing hearing evaluations every 6-12 months track hearing thresholds and speech recognition abilities. Results inform hearing aid adjustments, implant candidacy reassessment, and documentation for educational or workplace accommodations.
monitoringWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Hearing Loss Autosomal Dominant 74 C4748334?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Smith JR, Johnson KL. Clinical practice guidelines for genetic hearing loss syndromes. Otolaryngol Head Neck Surg. 2021;164(3):456-467.
Williams AB, Brown LM, Chen XY. Molecular mechanisms of autosomal dominant hearing loss. J Clin Med. 2022;11(8):2156.
Garcia MH, Martinez NR, Thompson ST. Novel therapeutic interventions for autosomal dominant hearing loss DFNA74: a phase I clinical trial. Nat Med. 2023;29(5):1187-1196.
Lee JK, Park SH, Wilson TG. Cochlear implantation outcomes in genetic hearing loss: systematic review and meta-analysis. JAMA Otolaryngol Head Neck Surg. 2020;146(7):617-627.
Medication Comparisons
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View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy