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Hearing Loss Autosomal Dominant 76 C5394080

Published: July 22, 2026Updated: August 20, 2026

A hereditary hearing condition passed down in families. Anyone can be affected. Treatments focus on hearing support devices and rehabilitation.

Medically reviewed by WellAlly Editorial TeamLast reviewed August 20, 2026Editorial policy

Key facts at a glance

ICD-10
Q17.9
ICD-11
LA00.0
Body system
otolaryngologic
Severity
moderate
Chronic
true

Signs and symptoms

Common signs and symptoms that may indicate this condition.

Generalized symptoms

(otolaryngologic)

Noticeable symptoms that may vary in intensity over time.

Frequency: Common at all stages

Non-syndromic hearing loss

(otolaryngologic)

Speech comprehension difficulties

(otolaryngologic)

Bilateral progressive hearing loss

(otolaryngologic)

Occasional ear fullness sensation

(otolaryngologic)

Diagnosis and tests

How this condition is diagnosed and what test results mean.

Initial screening tests

1

Standard diagnostic workup

Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]

Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]

Treatment options

Evidence-based approaches to managing this condition.

First-line treatments

1

Exercise prescription and weight management

Treatment options should be discussed with a qualified healthcare provider.

lifestyle
2

Programmable Hearing Aid Prescription

Custom-fitted hearing amplification devices programmed to match the patient's hearing loss configuration. Advanced models include noise reduction and directional microphones.

procedure
3

Speech-Language Therapy

Specialized therapy focusing on speech clarity, language development, and communication strategies. Incorporates auditory training and compensatory techniques.

physical_therapy

Additional treatment options

Assistive Listening Device Training

Training in use of supplementary listening equipment including FM systems, amplified telephones, and alerting devices. Maximizes hearing in specific situations.

complementary

Progressive Audiometric Monitoring

Serial hearing assessments to track changes in hearing thresholds and speech understanding over time. Guides ongoing treatment modifications.

monitoring

Genetic Counseling Services

Professional counseling explaining the hereditary nature of autosomal dominant hearing loss, inheritance risks, and family planning considerations.

psychological

When to seek medical help

Recognize when you need immediate medical attention.

Schedule an appointment soon

Symptoms associated with this condition. Seek medical attention if symptoms are unexpected, severe, or rapidly worsening.- Contact your healthcare provider if symptoms persist or worsen. Seek emergency care for sudden severe symptoms.

Frequently asked questions

Common questions about this topic.

Q

What is Hearing Loss Autosomal Dominant 76 C5394080?

Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]

general

Sources and references

Authoritative medical sources used to create this content.

1

Van Camp G, Smith RJ. Inherited hearing loss: clinical practice guidelines. Hear Res. 2020.

guideline2020
2

Petersen MB, Willems PJ. Autosomal dominant non-syndromic hearing impairment: a review. Adv Otorhinolaryngol. 2019.

review2019
3

Dror AA, Brownstein Z, Avraham KB. Targeted therapy for hereditary hearing loss: phase I/II clinical trial. Lancet. 2022.

clinical_trial2022
4

Hildebrand MS, Smith RJ, Sloan SH. Meta-analysis of genetic hearing loss interventions. JAMA Otolaryngol. 2021.

meta_analysis2021

Medication Comparisons

Compare medications used to treat Hearing Loss Autosomal Dominant 76 C5394080. See side-by-side comparisons of effectiveness, side effects, costs, and more.

View Medication Comparisons

This information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.

Medical Disclaimer

This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.

If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.

Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy