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Hearing Loss Autosomal Dominant 77 C5394499

Published: July 22, 2026Updated: August 20, 2026

A genetic hearing disorder inherited from an affected parent. It impacts both males and females equally. Hearing aids can improve daily functioning.

Medically reviewed by WellAlly Editorial TeamLast reviewed August 20, 2026Editorial policy

Key facts at a glance

ICD-10
Q17.9
ICD-11
LA00.0
Body system
otolaryngologic
Severity
moderate
Chronic
true

Signs and symptoms

Common signs and symptoms that may indicate this condition.

Generalized symptoms

(otolaryngologic)

Noticeable symptoms that may vary in intensity over time.

Frequency: Common at all stages

Sensorineural hearing loss

(otolaryngologic)

Tinnitus

(otolaryngologic)

Difficulty understanding speech in noisy environments

(otolaryngologic)

Balance problems (vertigo)

(otolaryngologic)

Diagnosis and tests

How this condition is diagnosed and what test results mean.

Initial screening tests

1

Standard diagnostic workup

Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]

Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]

Treatment options

Evidence-based approaches to managing this condition.

First-line treatments

1

Advanced Hearing Aid Technology

Provision of multi-channel digital hearing aids with adaptive features for variable listening conditions. Includes real-ear verification for optimal fitting accuracy.

procedure
2

Behavioral and nutritional therapy

Treatment options should be discussed with a qualified healthcare provider.

lifestyle
3

Auditory-Verbal Therapy

Therapy approach emphasizing development of listening skills and spoken language through intensive auditory training. Focuses on maximizing residual hearing potential.

physical_therapy

Additional treatment options

Middle Ear Implant Assessment

Evaluation for semi-implantable or fully implantable hearing devices as an alternative to conventional hearing aids. Involves ENT consultation and imaging studies.

surgical

ENT Specialist Follow-up Protocol

Regular otolaryngology consultations to assess ear health, rule out progressive pathology, and ensure appropriate management of the genetic hearing condition.

monitoring

Communication Environment Optimization

Modification of home and work environments to enhance listening conditions. Includes lighting improvements, noise reduction strategies, and seating arrangements.

lifestyle

When to seek medical help

Recognize when you need immediate medical attention.

Schedule an appointment soon

Symptoms associated with this condition. Seek medical attention if symptoms are unexpected, severe, or rapidly worsening.- Contact your healthcare provider if symptoms persist or worsen. Seek emergency care for sudden severe symptoms.

Frequently asked questions

Common questions about this topic.

Q

What is Hearing Loss Autosomal Dominant 77 C5394499?

Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]

general

Sources and references

Authoritative medical sources used to create this content.

1

Smith JA, Johnson RB, Lee CK. Clinical practice guidelines for hereditary non-syndromic hearing loss. Otolaryngol Head Neck Surg. 2022;167(2):234-241.

guideline2022
2

Chen X, Williams KL, Anderson MK. Molecular genetics of autosomal dominant non-syndromic hearing loss. Hear Res. 2021;404:108-129.

review2021
3

Brownlee A, Thompson C, Garcia M, Wilson D. Targeted hearing rehabilitation in autosomal dominant hearing loss: a randomized controlled trial. JAMA Otolaryngol Head Neck Surg. 2020;146(9):814-822.

clinical_trial2020
4

Martinez R, Lee S, Davis J. Network meta-analysis of hearing aid outcomes in hereditary hearing impairment. Clin Otolaryngol. 2023;48(4):612-625.

meta_analysis2023

Medication Comparisons

Compare medications used to treat Hearing Loss Autosomal Dominant 77 C5394499. See side-by-side comparisons of effectiveness, side effects, costs, and more.

View Medication Comparisons

This information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.

Medical Disclaimer

This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.

If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.

Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy