Heterotaxy Visceral 3 Autosomal C1853444
An inherited disorder affecting organ positioning in the body. It follows autosomal recessive inheritance and involves complex heart and organ malformations. Multidisciplinary care and surgery are often necessary.
Key facts at a glance
- ICD-10
- Q89.9
- ICD-11
- LA00.0
- Body system
- congenital
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Dextrocardia
(cardiovascular)Generalized symptoms
(congenital)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Atrial isomerism
(cardiovascular)Polysplenia
(gastrointestinal)Cerebral malformations
(nervous)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Complex Cardiac Surgery
Surgical intervention to correct structural heart defects associated with heterotaxy, including repair of abnormal venous connections and valve abnormalities. Typically performed in infancy or early childhood depending on severity.
Medication management with follow-up
Active treatment with regular monitoring by a healthcare provider is recommended.
Cardiac Imaging Surveillance
Regular echocardiograms, CT scans, and MRI monitoring to track cardiac structure and function over time. Essential for detecting changes in organ arrangement and function.
Additional treatment options
Cardiac Catheterization
Interventional catheterization procedures to assess hemodynamics, close septal defects, or stent narrowed vessels. Used both diagnostically and therapeutically.
procedureCardiac Medication Management
Pharmacologic management including anticoagulation, antiarrhythmics, or heart failure medications as indicated by cardiac function. Dosages adjusted based on weight and organ function.
medicationPsychosocial Support Services
Counseling and support services for patients and families managing chronic cardiac conditions. Addresses anxiety, depression, and adjustment to living with a complex congenital condition.
psychologicalWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Heterotaxy Visceral 3 Autosomal C1853444?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalMedication Comparisons
Compare medications used to treat Heterotaxy Visceral 3 Autosomal C1853444. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy