Hydrocephalus Congenital Communicating 1 C5231454
A condition present from birth where cerebrospinal fluid accumulates in the brain ventricles without obstruction. It may cause head enlargement, developmental delays, and requires surgical placement of a shunt to drain fluid.
Key facts at a glance
- ICD-10
- G40.909
- ICD-11
- 8A00.0
- Body system
- neurologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(neurologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
CSF diversion procedure
Ventriculoperitoneal shunting is the primary surgical intervention to divert excess cerebrospinal fluid from the ventricles to the peritoneal cavity, reducing intracranial pressure and allowing normal brain development.
Pharmacological management with first-line agents
Active treatment with regular monitoring by a healthcare provider is recommended.
Neuroimaging surveillance
Regular head circumference measurements and imaging studies including ultrasound, CT, or MRI to assess ventricular size, brain development, and shunt function over time.
Additional treatment options
Medical intracranial pressure management
Temporary use of acetazolamide or other agents to reduce CSF production may be used pre-operatively or in select cases. Surgical intervention typically provides more definitive management.
medicationDevelopmental motor therapy
Physical therapy focusing on developmental milestones, muscle tone management, and motor skill development appropriate to the child's age and neurological status.
physical_therapyNeurodevelopmental and family support
Developmental pediatrics and psychology services to monitor cognitive development, provide family counseling, and address learning or behavioral needs that may emerge despite treatment.
psychologicalWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Hydrocephalus Congenital Communicating 1 C5231454?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalMedication Comparisons
Compare medications used to treat Hydrocephalus Congenital Communicating 1 C5231454. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 27, 2026. · Read our editorial policy