Hyperinsulinemic Hypoglycemia Familial 1 C2931832
An inherited disorder causing the pancreas to release too much insulin, leading to dangerously low blood sugar. Symptoms typically appear in infancy or early childhood. Management involves frequent feedings and medications to reduce insulin.
Key facts at a glance
- ICD-10
- E34.9
- ICD-11
- 5A00.0
- Body system
- endocrine
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Fatigue or weight changes
(endocrine)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Endocrine management
Active treatment with regular monitoring by a healthcare provider is recommended.
Frequent Small Meals Protocol
A structured eating plan involving 6-8 small meals throughout the day with complex carbohydrates and protein to maintain stable blood glucose levels and prevent hypoglycemia episodes.
Potassium Channel Activator Therapy
Medication that inhibits insulin secretion from pancreatic beta cells by keeping potassium channels open, thereby raising blood glucose levels and preventing dangerous hypoglycemic episodes.
Additional treatment options
Somatostatin Analog Injection
Synthetic hormone analog that suppresses insulin secretion through multiple mechanisms, providing glycemic control when first-line therapies are insufficient.
medicationContinuous Glucose Monitoring System
Real-time glucose tracking device that alerts caregivers to impending hypoglycemic episodes, allowing proactive intervention before dangerous blood sugar drops occur.
monitoringPartial Pancreatectomy
Surgical removal of a portion of the pancreas to reduce insulin-secreting tissue when medical management fails to prevent severe hypoglycemic episodes.
surgicalWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Hyperinsulinemic Hypoglycemia Familial 1 C2931832?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
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This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy