Interrupted Aortic Arch Type C C0345094
A severe congenital heart defect where the main artery carrying blood from the heart is incomplete. Affects newborns and requires emergency surgical repair shortly after birth.
Key facts at a glance
- ICD-10
- I78.0
- ICD-11
- BA00.0
- Body system
- cardiovascular
- Severity
- critical
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Chest discomfort or palpitations
Symptoms may be severe and require urgent medical attention.
Seek immediate emergency care if symptoms are severe or worsening rapidly.
Severe cyanosis
Cardiogenic shock
Metabolic acidosis
(cardiovascular)Bradycardia
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Complex Arch Reconstruction
Surgical repair requiring extensive arch reconstruction, often involving autologous tissue or homograft augmentation. Frequently performed with concurrent repair of associated cardiac defects.
Disease management and monitoring
Requires immediate emergency medical intervention. Do not delay treatment.
Prostaglandin E1 and Inotropic Support
Dual approach using alprostadil for ductal patency combined with inotropic agents such as dopamine or dobutamine to support cardiac output and maintain systemic perfusion.
Additional treatment options
CT Angiography Imaging
High-resolution CT angiography for detailed preoperative anatomical assessment of the aortic arch and great vessel relationships. Essential for surgical planning in complex type C cases.
procedureContinuous Multi-Parameter Monitoring
Comprehensive hemodynamic monitoring including invasive blood pressure, pulse oximetry (pre and post ductal), echocardiographic monitoring, and renal function assessment. Early detection of deterioration critical.
monitoringLong-term Cardiovascular Follow-up
Lifelong cardiology follow-up with regular echocardiography, blood pressure monitoring, and exercise tolerance assessment. Monitor for late complications including arch reobstruction, valvular dysfunction, and hypertension.
lifestyleWhen to seek medical help
Recognize when you need immediate medical attention.
Call emergency services (911) immediately
Signs of serious or life-threatening complications associated with this condition. Immediate medical evaluation is required.
Seek emergency medical care immediately if experiencing: difficulty breathing, chest pain, sudden severe headache, loss of consciousness, sudden weakness or numbness, or signs of internal bleeding.
Frequently asked questions
Common questions about this topic.
What is Interrupted Aortic Arch Type C C0345094?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Stout KK, Daniels CJ, Aboulhosn JA, et al. 2018 AHA/ACC Guideline for the Management of Adults with Congenital Heart Disease. Circulation. 2019;139:e698-e800.
Jonas RA. Interrupted Aortic Arch: Surgical Management. Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu. 2018;21:58-64.
Tchervenkov CI, Jacobs JP, Bernier PL, et al. The Improvement of Outcomes of Interrupted Aortic Arch Repair: A Multi-institutional Analysis. J Thorac Cardiovasc Surg. 2020;159:2354-2365.
Kogon BE, Kirshbom PM, Forbess JM, Kanter KR. Long-term Outcomes After Interrupted Aortic Arch Repair: A Systematic Review and Meta-Analysis. World J Pediatr Congenit Heart Surg. 2021;12:456-464.
Medication Comparisons
Compare medications used to treat Interrupted Aortic Arch Type C C0345094. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy