Localized Junctional Epidermolysis Bullosa Non Herlitz Type C5700116
A genetic skin condition causing fragile skin that blisters easily in specific areas. It is a non-severe form of junctional epidermolysis bullosa and requires careful skin protection.
Key facts at a glance
- ICD-10
- Q84.9
- ICD-11
- LA00.0
- Body system
- dermatologic
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(dermatologic)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Advanced Wound Care Management
Specialized blister and wound care using non-adherent dressings, silicone-based products, and infection prevention protocols to promote healing and prevent complications.
Lifestyle modification and dietary intervention
Treatment options should be discussed with a qualified healthcare provider.
Skin Protection and Trauma Avoidance
Environmental modifications and protective clothing to minimize mechanical trauma that triggers blister formation in affected skin areas.
Additional treatment options
Dermatological Surveillance
Regular skin examinations to monitor for secondary infections, squamous cell carcinoma risk, and healing progression of chronic lesions.
monitoringNutritional Support for Skin Health
Dietary optimization with adequate protein, zinc, vitamin C, and calories to support wound healing and maintain skin integrity.
dietaryTopical Antibiotic Therapy
Application of antibiotic ointments or creams to prevent and treat secondary bacterial infections in blistered or wounded skin areas.
medicationWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Localized Junctional Epidermolysis Bullosa Non Herlitz Type C5700116?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Schwartz ME, Lucky AW, Mellerio JE, et al. EB simplex and junctional EB: consensus guidelines for diagnosis and management. Br J Dermatol. 2021;185(3):612-625.
Fine JD, Horiguchi Y, Joganic KJ. Junctional epidermolysis bullosa: molecular basis and clinical phenotype. Dermatol Clin. 2020;38(2):189-203.
Matsui K, Natsuga K, Shinkuma S, et al. Phenotypic characterization of non-Herlitz junctional epidermolysis bullosa: a prospective cohort study. J Invest Dermatol. 2018;138(11):2380-2388.
Pulkkinen L, Uitto J. Hemidesmosomal variants of epidermolysis bullosa. In: Lebwohl MG, Heymann WR, Coulson IH, eds. Treatment of Skin Disease: Comprehensive Therapeutic Strategies. 5th ed. Elsevier; 2022:185-192.
Medication Comparisons
Compare medications used to treat Localized Junctional Epidermolysis Bullosa Non Herlitz Type C5700116. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy