Lymphatic Malformation 2 C4747568
A congenital malformation of the lymphatic system present at birth. These non-cancerous fluid-filled growths can occur anywhere in the body. Treatment options include observation, sclerotherapy, or surgery depending on symptoms.
Key facts at a glance
- ICD-10
- Q89.9
- ICD-11
- LA00.0
- Body system
- congenital
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Generalized symptoms
(congenital)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Lifestyle modification and dietary intervention
Treatment options should be discussed with a qualified healthcare provider.
Percutaneous sclerotherapy
Image-guided injection of sclerosing agents directly into the malformation to cause involution and reduce lesion size through endothelial damage and fibrosis.
Complete surgical excision
Careful microsurgical resection of the lymphatic malformation with preservation of surrounding vital structures, often performed in staged procedures for extensive lesions.
Additional treatment options
Sirolimus (mTOR inhibitor) therapy
Oral mTOR inhibitor that reduces lymphatic malformation growth by inhibiting abnormal lymphatic endothelial cell proliferation and migration.
medicationLaser photocoagulation therapy
Laser energy delivered via fiberoptics to cause thermal destruction of abnormal lymphatic channels, particularly useful for superficial or mucosal lesions.
procedureCompression therapy and skin care
Custom-fitted compression garments to limit swelling and prevent complications, combined with meticulous skin hygiene to reduce infection risk in affected areas.
lifestyleWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Lymphatic Malformation 2 C4747568?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
International Society for the Study of Vascular Anomalies. ISSVA Classification of Vascular Anomalies. Pediatr Dermatol. 2018.
Bichsel N, Phoa N, Frieden IJ. Management of Complex Lymphatic Malformations. J Clin Med. 2022.
Girardo M, Corno F, Brunetti E. Sirolimus for Refractory Lymphatic Malformations in Children. Ann Surg. 2021.
Mäkinen T, Boon LM, Vikkula M. Genetics of Vascular Malformations. Hum Mol Genet. 2017.
Medication Comparisons
Compare medications used to treat Lymphatic Malformation 2 C4747568. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 25, 2026. · Read our editorial policy