Maturity Onset Diabetes Of The Young Type 13 C4225365
A rare genetic type of diabetes caused by mutations in the KCNJ11 gene that affects how insulin is released from pancreatic beta cells. Usually diagnosed in adolescence or early adulthood. Management varies based on individual needs.
Key facts at a glance
- ICD-10
- E34.9
- ICD-11
- 5A00.0
- Body system
- endocrine
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Fatigue or weight changes
(endocrine)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Polyuria
(endocrine)Polydipsia
(endocrine)Weight loss
(endocrine)Blurred vision
(endocrine)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Endocrine management
Treatment options should be discussed with a qualified healthcare provider.
Sulfonylurea therapy
First-line pharmacotherapy using sulfonylureas to stimulate insulin secretion from pancreatic beta cells. This approach is particularly effective for MODY types caused by HNF1A and HNF4A mutations.
Carbohydrate-controlled diet
Structured meal planning with consistent carbohydrate intake distributed across meals to maintain stable glucose levels. Focus on low glycemic index foods and complex carbohydrates.
Additional treatment options
Continuous glucose monitoring
Regular monitoring of blood glucose levels using CGM devices or self-monitoring to track glycemic patterns and adjust treatment accordingly.
monitoringRegular physical activity
Structured exercise program including aerobic activities and resistance training to improve insulin sensitivity and glycemic control.
lifestyleGenetic counseling
Specialized counseling to understand the hereditary nature of MODY, family screening implications, and reproductive considerations.
complementaryWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Maturity Onset Diabetes Of The Young Type 13 C4225365?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
American Diabetes Association. Standards of Care in Diabetes—2023. Diabetes Care. 2023.
Naylor R, Shields RL, Ellard S. Genetic testing and molecular diagnostics in monogenic diabetes. Diabet Med. 2022.
Brenner C, Fischer M, Hattersley AT. Clinical characterization and genetic analysis of MODY in a large European cohort. J Clin Endocrinol Metab. 2021.
Zhang H, Wang W, Liu L. Molecular mechanisms and treatment outcomes of HNF1A and HNF4A-related MODY: A systematic review. Endocr Rev. 2020.
Medication Comparisons
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This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy