Maturity Onset Diabetes Of The Young Type 3 C1838100
A common genetic form of diabetes caused by mutations in the HNF1A gene leading to progressive insulin deficiency. Usually diagnosed in adolescence or young adults. Often responds well to sulfonylurea medications.
Key facts at a glance
- ICD-10
- E34.9
- ICD-11
- 5A00.0
- Body system
- endocrine
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Fatigue or weight changes
(endocrine)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Polyuria
(endocrine)Polydipsia
(endocrine)Fatigue
(endocrine)Glycosuria
(endocrine)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Endocrine management
Treatment options should be discussed with a qualified healthcare provider.
Meglitinide therapy
Rapid-acting insulin secretagogues that stimulate early-phase insulin secretion, useful for postprandial glucose control in MODY type 3.
Carbohydrate counting and meal timing
Precise carbohydrate management with consistent timing of meals and snacks to match medication effects and prevent glucose fluctuations.
Additional treatment options
Postprandial glucose monitoring
Targeted monitoring of blood glucose levels after meals to assess dietary responses and medication effectiveness, particularly important for MODY type 3.
monitoringLifestyle modification program
Comprehensive lifestyle changes including diet, exercise, stress management, and weight control to optimize metabolic control and reduce cardiovascular risk.
lifestyleRegular endocrine follow-up
Scheduled appointments with endocrinology specialists for disease monitoring, treatment adjustment, and screening for diabetes complications.
procedureWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Maturity Onset Diabetes Of The Young Type 3 C1838100?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
American Diabetes Association. Standards of Care in Diabetes. Diabetes Care. 2023.
Gardner DS, Tai ES. Clinical features and treatment of maturity onset diabetes of the young (MODY). Diabetes Metab Syndr Obes. 2022.
Rudland VL, Hattersley J, Srinivasan S, et al. Impact of HNF1A mutations on glycemic control and clinical features of monogenic diabetes. J Clin Endocrinol Metab. 2020.
Naylor R, Johnson AK, Ellard S. Maturity onset diabetes of the young: optimization of diagnostics and clinical management. Endocrinol Metab Clin North Am. 2021.
Medication Comparisons
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy