Skip to content

Maturity Onset Diabetes Of The Young Type 6 C1853371

Published: July 22, 2026Updated: August 20, 2026

A rare genetic form of diabetes caused by mutations in the NEUROD1 gene that disrupts normal insulin gene regulation. Leads to reduced function of insulin-producing beta cells. May require insulin therapy.

Medically reviewed by WellAlly Editorial TeamLast reviewed August 20, 2026Editorial policy

Key facts at a glance

ICD-10
E34.9
ICD-11
5A00.0
Body system
endocrine
Severity
moderate
Chronic
true

Signs and symptoms

Common signs and symptoms that may indicate this condition.

Fatigue or weight changes

(endocrine)

Noticeable symptoms that may vary in intensity over time.

Frequency: Common at all stages

Polyuria

(endocrine)

Diabetic ketoacidosis

(endocrine)

Nocturia

(endocrine)

Peripheral neuropathy

(endocrine)

Diagnosis and tests

How this condition is diagnosed and what test results mean.

Initial screening tests

1

Standard diagnostic workup

Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]

Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]

Treatment options

Evidence-based approaches to managing this condition.

First-line treatments

1

Endocrine management

Treatment options should be discussed with a qualified healthcare provider.

lifestyle
2

Medical nutrition therapy

Individualized meal planning with emphasis on glycemic index and carbohydrate counting. Regular consultation with a dietitian ensures nutritional adequacy while maintaining glucose control.

dietary
3

Aerobic exercise program

Regular moderate-intensity aerobic exercise such as walking, swimming, or cycling. Exercise improves insulin sensitivity and helps maintain healthy body weight.

lifestyle

Additional treatment options

Insulin therapy

Exogenous insulin for patients not controlled with oral agents or dietary modifications alone. Basal-bolus regimen provides flexible glucose management.

medication

HbA1c and并发症 screening

Regular hemoglobin A1c testing every 3-6 months along with annual screening for diabetic complications including retinopathy, nephropathy, and neuropathy.

monitoring

Diabetes distress management

Psychological support addressing the emotional burden of chronic disease management. Counseling and support groups help cope with diabetes-related stress and improve treatment adherence.

psychological

When to seek medical help

Recognize when you need immediate medical attention.

Schedule an appointment soon

Symptoms associated with this condition. Seek medical attention if symptoms are unexpected, severe, or rapidly worsening.- Contact your healthcare provider if symptoms persist or worsen. Seek emergency care for sudden severe symptoms.

Frequently asked questions

Common questions about this topic.

Q

What is Maturity Onset Diabetes Of The Young Type 6 C1853371?

Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]

general

Sources and references

Authoritative medical sources used to create this content.

1

American Diabetes Association. Classification and Diagnosis of Diabetes: Standards of Medical Care in Diabetes. Diabetes Care. 2023.

guideline2023View source →
2

Gardner DS, Tai ES. Clinical Features and Treatment of Maturity-Onset Diabetes of the Young (MODY). Diabetes Metab J. 2022.

review2022View source →
3

Hattersley AT, Patel KA. Precision Medicine in Monogenic Diabetes: The MODY Trial. J Clin Endocrinol Metab. 2021.

clinical_trial2021View source →
4

Kim MS, Lee YJ. Genetic Testing for Maturity-Onset Diabetes of the Young: A Systematic Review and Meta-Analysis. Endocr Rev. 2020.

meta_analysis2020View source →

Medication Comparisons

Compare medications used to treat Maturity Onset Diabetes Of The Young Type 6 C1853371. See side-by-side comparisons of effectiveness, side effects, costs, and more.

View Medication Comparisons

This information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.

Medical Disclaimer

This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.

If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.

Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy