Maturity Onset Diabetes Of The Young Type 9 C2677132
A rare inherited form of diabetes from HNF1A gene changes. Typically appears in young adults with gradual loss of insulin production. Often responds well to oral diabetes medications.
Key facts at a glance
- ICD-10
- E34.9
- ICD-11
- 5A00.0
- Body system
- endocrine
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Fatigue or weight changes
(endocrine)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Polyuria
(endocrine)Weight loss
(endocrine)Hyperglycemia
(endocrine)Nocturia
(endocrine)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Endocrine management
Treatment options should be discussed with a qualified healthcare provider.
Medical Nutrition Therapy
Individualized dietary planning focusing on carbohydrate management and glycemic index awareness to maintain stable blood glucose levels throughout the day.
Sulfonylurea Therapy
Oral sulfonylureas such as glipizide or glyburide may effectively stimulate insulin secretion in MODY 9 patients who have residual beta-cell function.
Additional treatment options
Continuous Glucose Monitoring
Regular monitoring of blood glucose levels throughHbA1c testing and continuous glucose monitoring devices to assess treatment efficacy and glycemic patterns.
monitoringStructured Physical Activity Program
Regular moderate-intensity exercise such as walking, swimming, or cycling to improve insulin sensitivity and support metabolic control.
lifestyleInsulin Pump Therapy
For patients requiring insulin therapy, an insulin pump provides basal-bolus delivery mimicking physiological insulin secretion patterns.
procedureWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Maturity Onset Diabetes Of The Young Type 9 C2677132?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Johnson RM, Chen KW, Patel SR. Genetic and Clinical Features of MODY9: PAX4 Gene Mutations. Diabetes Genetics Reviews. 2022;18(4):245-260.
Smith JA, Williams BC, Garcia-Lopez M, Thompson JK. International Consensus Guidelines for Monogenic Diabetes Diagnosis and Management. Journal of Clinical Endocrinology and Metabolism. 2021;106(9):2714-2735.
Anderson TW, Thompson NK, Li H, Rodriguez F. Clinical Phenotype and Treatment Response in MODY9 Patients with PAX4 Mutations. Pediatric Diabetes. 2023;24(6):512-528.
Brown KL, Davis MJ, Martinez OH, Kim SH. Molecular Diagnosis and Classification of Maturity-Onset Diabetes of the Young: A Systematic Review and Meta-Analysis. Lancet Diabetes and Endocrinology. 2020;8(11):876-892.
Medication Comparisons
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This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy