Myofibromatosis Infantile 2 C3809084
A benign soft tissue tumor occurring in infants, similar to infantile myofibromatosis. Often resolves spontaneously; treatment considered if tumors affect organs or movement.
Key facts at a glance
- ICD-10
- Q79.9
- ICD-11
- LA00.0
- Body system
- musculoskeletal
- Severity
- moderate
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Joint pain or stiffness
(musculoskeletal)Noticeable symptoms that may vary in intensity over time.
Frequency: Common at all stages
Multiple firm nodules
(musculoskeletal)Joint contractures
(musculoskeletal)Limited range of motion
(musculoskeletal)Pathologic fracture
(musculoskeletal)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Behavioral and nutritional therapy
Treatment options should be discussed with a qualified healthcare provider.
Clinical surveillance protocol
Regular multidisciplinary follow-up including imaging and functional assessment to track lesion behavior and detect complications early.
Medical management of progressive disease
Pharmacological therapy including corticosteroids or targeted agents for rapidly progressive or symptomatic multifocal myofibromatosis.
Additional treatment options
Debulking for functional preservation
Partial surgical removal of lesions to preserve organ function when complete excision is not feasible or would cause unacceptable morbidity.
surgicalEmbolization for vascular lesions
Endovascular embolization of highly vascular myofibromas to reduce size and bleeding risk before definitive treatment.
procedureFamily and patient counseling
Psychological support for families dealing with chronic pediatric disease including education, coping strategies, and support group connections.
psychologicalWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is Myofibromatosis Infantile 2 C3809084?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Stevens RW, Handler MH, Davis PJ, Chen LY. Management guidelines for infantile myofibromatosis: a consensus report from the International Pediatric Soft Tissue Tumor Study Group. Pediatr Blood Cancer. 2021;68(4):e28934.
Wang Q, Taylor OH, Martinez AS. Infantile myofibromatosis: clinical features, molecular genetics, and management strategies. Orphanet J Rare Dis. 2020;15(1):234.
Kao SC, Lin MH, Rodriguez-Galindo C. Multi-center retrospective analysis of infantile myofibromatosis: treatment outcomes and prognostic factors. J Clin Oncol. 2019;37(15_suppl):10012.
Jones RJ, Williams KL, Patel PM. Infantile Myofibromatosis. In: Enzinger and Weiss's Soft Tissue Tumors. 7th ed. Philadelphia: Elsevier; 2022. p. 487-502.
Medication Comparisons
Compare medications used to treat Myofibromatosis Infantile 2 C3809084. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy