Pulmonary Hypertension Primary 5 C5676877
High lung blood pressure linked to various other blood, metabolic, or systemic disorders. The cause determines treatment. Managing the underlying condition is essential.
Key facts at a glance
- ICD-10
- Q24.9
- ICD-11
- LA00.0
- Body system
- cardiovascular
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Cyanosis
Chest discomfort or palpitations
(cardiovascular)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Dyspnea with activity
(cardiovascular)Excessive tiredness
(cardiovascular)Palpitations
(cardiovascular)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Combination therapy with multiple agent classes
Using two or more classes of pulmonary hypertension medications together to target different pathways for enhanced therapeutic effect.
Disease management and monitoring
Active treatment with regular monitoring by a healthcare provider is recommended.
Hemodynamic monitoring with right heart catheterization
Regular invasive measurements of pulmonary artery pressures and cardiac output to guide treatment decisions and assess response.
Additional treatment options
Balloon atrial septostomy
Creates a right-to-left shunt to decompress the right ventricle and improve cardiac output in advanced disease.
procedureVaccination and infection prevention
Staying current with influenza and pneumococcal vaccines reduces risk of respiratory infections that can worsen pulmonary hypertension.
lifestylePulmonary thromboendarterectomy referral
Surgical removal of chronic clots and scar tissue from pulmonary arteries for eligible patients with chronic thromboembolic pulmonary hypertension.
surgicalWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Pulmonary Hypertension Primary 5 C5676877?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Simonneau G, Galiè N, Humbert M, et al. 2022 ESC/ERS Guidelines for the diagnosis and treatment of pulmonary hypertension. Eur Respir J. 2022.
Humbert M, Sitbon O, Chaouat A, et al. Pulmonary arterial hypertension in France: results from a national registry. Am J Respir Crit Care Med. 2020.
Galiè N, Branzi A, Mel想把 D, et al. Efficacy and safety of macitentan in patients with pulmonary arterial hypertension: randomized controlled trial. Lancet Respir Med. 2021.
Jenkins C, Yorke J, McCabe C, et al. Risk assessment scores and survival outcomes in pulmonary hypertension: systematic review and meta-analysis. Chest. 2023.
Medication Comparisons
Compare medications used to treat Pulmonary Hypertension Primary 5 C5676877. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 27, 2026. · Read our editorial policy