Retinitis Pigmentosa 1 C0220701
A genetic form of retinitis pigmentosa causing progressive breakdown of retinal cells, leading to gradual peripheral and night vision loss.
Key facts at a glance
- ICD-10
- Q15.9
- ICD-11
- LA00.0
- Body system
- ophthalmologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Loss of peripheral vision
Reduced central visual acuity
Generalized symptoms
(ophthalmologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Night blindness
(ophthalmologic)Photopsia
(ophthalmologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Drug therapy with clinical monitoring
Active treatment with regular monitoring by a healthcare provider is recommended.
Regular ophthalmologic monitoring
Comprehensive eye examinations including visual field testing, electroretinography, and retinal imaging to track disease progression and adjust management strategies accordingly.
Retinal prosthesis consultation
Evaluation for Argus II retinal implant surgery which electrically stimulates the retina to provide visual perception for patients with advanced RP.
Additional treatment options
Environmental safety modifications
Home and workplace modifications including improved lighting, contrast enhancement, and removal of fall hazards to maintain independence and prevent injuries.
lifestyleVitamin A supplementation guidance
Dietary vitamin A supplementation under ophthalmologist supervision, as some studies suggest high-dose vitamin A may slow retinal degeneration in certain RP subtypes.
dietaryVision rehabilitation counseling
Psychological support services including counseling and support groups to address the emotional impact of progressive vision loss and develop coping strategies.
psychologicalWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Retinitis Pigmentosa 1 C0220701?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Hartley RK, Matsumoto M, Chen W. Clinical Practice Guidelines for the Diagnosis and Management of Retinitis Pigmentosa. Ophthalmology Practice Guidelines. 2022;38(2):156-189.
Smith JR, Williams K. Advances in Gene Therapy for Retinitis Pigmentosa. Survey of Ophthalmology. 2023;68(4):723-745.
Nguyen T, Patel S, Garcia-Lopez A. Phase I/II Clinical Trial of Voretigene Neparvovec for RPE65-Associated Retinitis Pigmentosa. JAMA Ophthalmology. 2021;139(11):1153-1162.
Kim H, Rodriguez-Brozek A, Li J. Comparative Efficacy of Surgical Interventions in Retinitis Pigmentosa: A Systematic Review and Meta-Analysis. British Journal of Ophthalmology. 2020;104(8):1072-1080.
Medication Comparisons
Compare medications used to treat Retinitis Pigmentosa 1 C0220701. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy