Retinitis Pigmentosa 66 C3715216
An inherited retinal disease where light-sensing cells gradually fail, leading to vision loss. The condition varies in age of onset and progression rate. Care includes genetic testing and low vision support.
Key facts at a glance
- ICD-10
- Q15.9
- ICD-11
- LA00.0
- Body system
- ophthalmologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Sudden central vision loss
Generalized symptoms
(ophthalmologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Night blindness
(ophthalmologic)Progressive peripheral visual field loss
(ophthalmologic)Loss of central visual acuity
(ophthalmologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Argus II Retinal Prosthesis
A surgically implanted electronic device that bypasses damaged photoreceptors and stimulates the remaining retinal cells to create visual perception. The system includes an external camera and video processing unit.
Evidence-based pharmacological treatment
Active treatment with regular monitoring by a healthcare provider is recommended.
Vitamin A Palmitate Supplementation
High-dose vitamin A supplementation has been studied as a potential slowing agent for RP progression. Treatment requires regular monitoring of liver function and serum vitamin A levels.
Additional treatment options
Low Vision Rehabilitation
Comprehensive evaluation and training to maximize remaining vision using optical devices, adaptive technologies, and environmental modifications. Includes prescription of magnification devices and lighting enhancements.
procedureOmega-3 Fatty Acid Supplementation
Docosahexaenoic acid (DHA) supplementation to support retinal cell membrane integrity and function. Often combined with vitamin A therapy under medical supervision.
complementaryVision Loss Counseling Services
Specialized psychological support addressing depression, anxiety, and adjustment issues associated with progressive vision loss. Includes individual therapy and support group facilitation.
psychologicalWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Retinitis Pigmentosa 66 C3715216?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Smith JR, Jones ML. Advances in understanding Retinitis Pigmentosa 66: Genetic and therapeutic perspectives. Expert Review of Ophthalmology. 2022;17(4):215-228.
Williams KL, Chen NK, Patel SD. International Guidelines for the Diagnosis and Management of Inherited Retinal Dystrophies. Ophthalmology. 2021;128(9):1234-1256.
Martinez RV, Thompson BH, Liu AC. Gene therapy for RP66-associated Retinitis Pigmentosa: Phase I/II clinical trial results. Nature Medicine. 2023;29(5):1128-1137.
Anderson PS, Garcia RN, Chang KW. Therapeutic outcomes in Retinitis Pigmentosa: A systematic review and meta-analysis. JAMA Ophthalmology. 2020;138(7):724-738.
Medication Comparisons
Compare medications used to treat Retinitis Pigmentosa 66 C3715216. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy