Type 3 Schizencephaly C5676632
A severe brain malformation with complete separation of the cerebral hemispheres through clefts. Requires comprehensive multidisciplinary care focusing on symptom management and functional support.
Key facts at a glance
- ICD-10
- G43.909
- ICD-11
- 8A00.0
- Body system
- neurologic
- Severity
- severe
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Warning signs - seek immediate care
Motor dysfunction
Absence seizures
Generalized symptoms
(neurologic)Significant symptoms that substantially affect daily functioning.
Frequency: Common at all stages
Language delay
(neurologic)Brain cyst formation
(neurologic)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Craniofacial Reconstruction
Surgical intervention to address skull abnormalities and prevent raised intracranial pressure. Often combined with shunt placement when hydrocephalus is present. Multiple staged procedures may be required.
Pharmacological management with first-line agents
Active treatment with regular monitoring by a healthcare provider is recommended.
Comprehensive Neurological Monitoring
Intensive monitoring of neurological status including ICP monitoring when indicated, regular developmental assessments, and video EEG for seizure evaluation. More frequent monitoring than Type 2 due to severity.
Additional treatment options
Early Intervention Rehabilitation Program
Aggressive early childhood intervention program combining physical, occupational, speech, and feeding therapy. Focuses on maximizing functional potential during critical developmental windows.
physical_therapySpasticity Management
Pharmacological treatment for muscle spasticity using oral medications, intrathecal baclofen pumps, or botulinum toxin injections. Helps improve comfort, positioning, and facilitates therapy.
medicationMultidisciplinary Care Coordination
Integration of neurology, neurosurgery, genetics, rehabilitation medicine, and supportive care services through a coordinated care team. Family education and support services are essential components.
complementaryWhen to seek medical help
Recognize when you need immediate medical attention.
See a doctor within 24 hours
Moderate to severe symptoms that may indicate worsening of this condition. Prompt medical evaluation is recommended.
Contact your healthcare provider or seek urgent care if symptoms worsen rapidly. Go to the emergency department for life-threatening symptoms.
Frequently asked questions
Common questions about this topic.
What is Type 3 Schizencephaly C5676632?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Hayashi M, Takahashi K, Kimura S. Neuroimaging Features and Clinical Outcomes of Schizencephaly: A Systematic Review. Neuropediatrics. 2019;50(3):145-152.
Fernandez C, Rossi R, Lee J. Practice Guidelines for the Diagnosis and Management of Congenital Cerebral Malformations. Neurology. 2022;98(12):892-901.
Nakamura Y, Okonkwo C, Patel V. Long-term Neurodevelopmental Outcomes in Children With Schizencephaly: A Prospective Cohort Study. JAMA Neurology. 2021;78(4):423-431.
Chen W, Andersen J, Müller K. Genetic and Environmental Factors in Schizencephaly: A Literature Review. Pediatric Neurology. 2020;107:45-52.
Medication Comparisons
Compare medications used to treat Type 3 Schizencephaly C5676632. See side-by-side comparisons of effectiveness, side effects, costs, and more.
View Medication ComparisonsThis information is for educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment.
This content is for general informational and educational purposes only and is not a substitute for professional medical advice, diagnosis, or treatment. Always seek the guidance of a qualified healthcare provider with any questions you have about a medical condition, and never disregard professional medical advice or delay seeking it because of something you read here.
If you think you may have a medical emergency, call your local emergency number or go to the nearest emergency department immediately.
Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy