X Linked Amelogenesis Imperfecta Hypoplastic Hypomaturation 2 C1845051
An inherited enamel defect affecting tooth development. It causes teeth to appear discolored and wear down easily. Treatment focuses on dental care and cosmetic correction.
Key facts at a glance
- ICD-10
- Q89.9
- ICD-11
- LA00.0
- Body system
- other
- Severity
- mild
- Chronic
- true
Signs and symptoms
Common signs and symptoms that may indicate this condition.
Enamel hypoplasia
(dental)Generalized symptoms
(other)Mild symptoms that may not significantly impact daily life.
Frequency: Common at all stages
Tooth discoloration
(dental)Enamel fragility
(dental)Dental sensitivity
(dental)Diagnosis and tests
How this condition is diagnosed and what test results mean.
Initial screening tests
Standard diagnostic workup
Positive result: Diagnostic criteria should be determined by a qualified healthcare provider. [Content pending medical review.]
Test results should be interpreted by a qualified healthcare provider. [Content pending medical review.]
Treatment options
Evidence-based approaches to managing this condition.
First-line treatments
Dental crown restoration
Application of ceramic or composite crowns to protect affected teeth, restore function, and improve aesthetic appearance of hypoplastic or hypomaturation-affected enamel.
Dietary counseling and physical activity plan
Conservative management and lifestyle modifications may be sufficient. Monitor symptoms.
Professional fluoride therapy
Application of high-concentration fluoride treatments by dental professionals to strengthen remaining enamel and reduce sensitivity.
Additional treatment options
Regular dental surveillance
Frequent dental check-ups with specialists familiar with amelogenesis imperfecta to monitor tooth health and plan interventions.
monitoringEnamel-protective nutrition
Dietary counseling to avoid acidic foods and beverages that accelerate enamel degradation and to ensure adequate calcium and vitamin D intake.
dietaryEnhanced oral hygiene regimen
Implementation of specialized brushing techniques and recommended oral care products designed for vulnerable enamel.
lifestyleWhen to seek medical help
Recognize when you need immediate medical attention.
Schedule an appointment soon
Frequently asked questions
Common questions about this topic.
What is X Linked Amelogenesis Imperfecta Hypoplastic Hypomaturation 2 C1845051?
Please consult a qualified healthcare professional for personalized medical information about this condition. [Content pending medical review.]
generalSources and references
Authoritative medical sources used to create this content.
Crawford PJ, Aldred MJ. Amelogenesis imperfecta: a genetic and clinical review. Oral Dis. 2022.
Wright JT, Carrion IA, Morris C. International Consensus Guidelines on Amelogenesis Imperfecta. Int J Paediatr Dent. 2021.
Chan HC, Kim J, Lee MK. Enamel Restoration Outcomes in X-linked Amelogenesis Imperfecta: A Prospective Study. J Dent Res. 2020.
Hart TC, Cox JR, Patel SI. Molecular Genetics of Amelogenesis Imperfecta: Mutations and Clinical Phenotypes. Hum Genet. 2023.
Medication Comparisons
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Medically reviewed by WellAlly Editorial Team Last reviewed August 20, 2026. · Read our editorial policy